This case presents a female patient in her thirties with progressive vision loss in the right eye secondary to choroidal neovascular membrane formation from a progressive retinal tumor. The retinal tumor carries characteristics of both choroidal osteoma and astrocytic hamartoma but does not fit the classic picture of either. Despite this dilemma of diagnosis, Anti-VEGF therapy is initiated in attempt to regress the CNVM and improve vision. Treatment outcomes are pending as the case is ongoing. Also, the patient was diagnosed with bilateral iris and retinal colobomas, microcornea and keratoconus which have implications for potential visual acuity outcomes and management.